This extension learning activity is designed to extend the learner and incorporate additional reading and research by the learner. Further reading and research is required from eTG, AMH, eMIMS and Stockley’s Drug Interactions.

Learning objectives

After successful completion of this CPD activity, pharmacists should be able to:

  • Define cystic fibrosis
  • Describe the pathophysiology of cystic fibrosis
  • Discuss the management of patients with cystic fibrosis
  • Identify the role of the pharmacist in managing a patient with cystic fibrosis.

Competency standards (2016) addressed: 1.1, 1.3, 1.4, 2.1, 2.3, 2.4, 3.2

Extended learning activity

After additional reading and research from recommended resources, pharmacists should be able to:

  • Identify drug-drug interactions and modify treatment regimens when managing people with cystic fibrosis
  • Assess the pharmacokinetic and pharmacodynamic properties of drugs used in cystic fibrosis when formulating treatment options
  • Discuss the drug treatment used for managing cystic fibrosis, including the management of adverse drug reactions.

Competency standards (2016) addressed: 1.1, 1.3, 1.4, 1.5, 2.2, 2.4, 3.1, 5.3

Already read the CPD in the journal? Scroll to the bottom to SUBMIT ANSWERS.  Read the full cystic fibrosis here.

Sarah is a 26-year-old female with this medical history:

  • Cystic fibrosis (F508del mutation)
  • Recurrent respiratory tract infections
  • Pancreatic insufficiency
  • GORD
  • Depression.

Sarah was diagnosed with CF at birth. Since Sarah’s transfer to the adult CF centre at

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